Hepatolenticular degeneration--is the term too narrow to explain Wilson's disease?

Wilson's Disease : A Case Report

Wilson's disease is a rare metabolic disorder involving copper metabolism may present with hepatic, neurological and psychiatric manifestations. We present a case of Wilson's disease with behavioral symptoms, which responded to risperidone.

Dimercaprol in the pre-neurological stage of Wilson's disease (hepatolenticular degeneration).

Review on Wilson's Disease

Surviving Wilson's disease.

[Whipple's triad as a clinical manifestation of hepatolenticular degeneration].

Hepatolenticular degeneration (Wilson's disease) is a rare condition characterised by a defect in biliary excretion of copper resulting in excessive copper accumulation and toxicity. To the most frequent symptoms of this disorder belong liver, neurological or psychiatric disturbances, although other less common clinical features may sometimes be present. Since the clinical presentation of the d...